Vulvar Paget Disease

Authors

  • Pakhanan Dankamak Department of Obstetrics and Gynecology, Faculty of Medicine, Prince of Songkla University, Hat Yai, Songkhla 90110, Thailand.
  • Kulisara Nanthamongkolkul Department of Obstetrics and Gynecology, Faculty of Medicine, Prince of Songkla University, Hat Yai, Songkhla 90110, Thailand.
  • Ingporn Jiamset Department of Obstetrics and Gynecology, Faculty of Medicine, Prince of Songkla University, Hat Yai, Songkhla 90110, Thailand.
  • Thiti Atjimakul Department of Obstetrics and Gynecology, Faculty of Medicine, Prince of Songkla University, Hat Yai, Songkhla 90110, Thailand.
  • Athithan Rattanaburi Department of Obstetrics and Gynecology, Faculty of Medicine, Prince of Songkla University, Hat Yai, Songkhla 90110, Thailand.

DOI:

https://doi.org/10.31584/psumj.2024264403

Keywords:

Extramammary Paget disease, Paget disease, vulva, vulvar lesion, vulvar neoplasm, vulvar Paget disease

Abstract

Vulvar Paget disease (VPD) is a rare and difficult-to-diagnose condition that can be associated with other types of cancer, such as urinary tract cancer and gastrointestinal tract cancer. Accurate and thorough diagnosis is essential. The main treatment for VPD is surgery, although alternative treatments are available in cases for which surgery is not feasible. These alternative treatments include radiation therapy, topical medications, and chemotherapy for advanced and disseminated cases. Due to the recurrent nature of VPD, continuous monitoring and follow-up are necessary. This article aimed to gather and explore information about VPD. The article includes the etiology of the disease, clinical characteristics, pathological features, various investigations, current treatment options for VPD.

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Published

2024-04-23

How to Cite

1.
Dankamak P, Nanthamongkolkul K, Jiamset I, Atjimakul T, Rattanaburi A. Vulvar Paget Disease. PSU Med J [Internet]. 2024 Apr. 23 [cited 2024 Nov. 20];4(1):25-34. Available from: https://he01.tci-thaijo.org/index.php/PSUMJ/article/view/264403

Issue

Vol. 4 No. 1 (2024): Jan-Apr

Section

Review Articles

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