Multiple Organs Thrombosis in Twin Children with Severe Protein C Deficiency
Keywords:
Severe protein C deficiency, ThrombosisAbstract
Abstract : 33 week-twin-children presented with purpuric lesion and were found to have multiple organ thrombosis. They were diagnosis as double heterozygous protein C deficiency. Quarantine plasma is another option to replace protein C while protein C concentrate is not available in Thailand.
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