ลักษณะทางคลินิกของผู้ป่วยโรค myelomeningocele ใน โรงพยาบาลศิริราชระหว่างปี พ.ศ. 2554-2555

ลักษณะทางคลินิกของผู้ป่วยโรค myelomeningocele ใน โรงพยาบาลศิริราชระหว่างปี พ.ศ. 2554-2555

Authors

  • ธนพร เอี่ยมพรรัตน์
  • วิลาวัณย์ ถิรภัทรพงศ์
  • กิ่งแก้ว ปาจรีย์

Keywords:

myelomeningocele, congenital anomaly, neural tube defect

Abstract

Objective: To study clinical characteristics of patients with myelomeningocele (MMC) in Siriraj Hospital.

Study design: Descriptive study

Setting: Medical record division, Siriraj Hospital

Subjects: All patients with MMC treated at Siriraj Hospital during 2011-2012.

Method: Retrospective review chart of all subjects

Results: One hundred sixteen chart of patients with MMC were studied. Forty seven percent of patients were children aged between 0-5 while 34 percent were children aged between 6-10. Hydrocephalus was the most associated clinical finding (36%). All of the total patients were divided into two groups. The first group was inpatients presenting with sacral or back mass that required surgical management (41%). The second group was outpatients presenting with complications

(59%). The most common complication was urinary complication(54%). Others were joint contractures or deformities, ambulationproblems and chronic wounds. Inpatients referred to rehabilitationdepartment received multidisciplinary care more than outpatients.Most patients who visited rehabilitation department had upper lumbar motor level (L1-L3) while the others had sacral motor level.

Conclusion: Most patients were children. There were outpatients more than inpatients. Several complications were found in many organ systems. Multidisciplinary clinic should be established in order to enable these patients to receive more appropriate treatments.

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