Dental Management for Alagille Syndrome: A Case Report

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Onauma Angwaravong
Rutchada Kittiprawong
Thidarat Angwarawong

Abstract

Alagille syndrome is a complex genetic disorders, having high variability in severity and multi-organ system involvement, with the presence of at least three out of five major systems: liver, heart, skeletal, eye, face, and some other organs may be involved. A multidisciplinary approach is needed to manage Alagille syndrome. Dental management for patient with Alagille syndrome could be different from healthy patients due to multi-organ disorders especially the impairments of liver function and congenital heart defects. Up to date, there are few articles addressing dental management for patients with Alagille syndrome. Thus, this article aims to review literatures related to Alagille syndrome regarding the etiology, incidence, clinical features, diagnosis, treatment, and dental management with case report.

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1.
Angwaravong O, Kittiprawong R, Angwarawong T. Dental Management for Alagille Syndrome: A Case Report. Khon Kaen Dent J [Internet]. 2019 Jun. 27 [cited 2023 Feb. 5];22(1):69-80. Available from: https://he01.tci-thaijo.org/index.php/KDJ/article/view/198593
Section
Clinical Science
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